Tuberous Sclerosis: A Review of 18 Cases
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چکیده
Tuberous sclerosis (TS) is an ectodermatosis of neurogenetic origin with variable neurological, cutaneous and visceral manifestations. TS is due to the development of benign tumors of the hamartomatous type. First described by Bourneville in 1880, the classic triad characterizing the TS was described by Vogt in 1908 including epilepsy, mental retardation and sebaceous adenomas. The prevalence is estimated between 1/6000 and 1/10000 population.
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